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Target
sublocation: Secreted Protein/Potential Cytokines.
Hexosaminidase B is the beta subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are encoded by separate genes. Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Beta subunit gene mutations lead to Sandhoff disease (GM2-gangliosidosis type II). Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, May 2014]
| Target ID |
GM-SE0260
|
| Target Name |
HEXB
|
Gene Group ldentifer (Target Gene ID in Homo
species)
|
3074
|
| Gene ID |
100073289 (Equus caballus), 15212 (Mus musculus), 294673 (Rattus norvegicus), 3074 (Homo sapiens) 478100 (Canis lupus familiaris), 493928 (Felis catus), 618571 (Bos taurus), 704464 (Macaca mulatta)
|
| Target Alternative Names |
Beta-N-acetylhexosaminidase subunit beta (Hexosaminidase subunit B),Beta-hexosaminidase subunit beta,Cervical cancer proto-oncogene 7 protein (HCC-7),ENC-1AS,HEL-248,HEL-S-111,HEXB,Hexb,N-acetyl-beta-glucosaminidase subunit beta
|
| Uniprot Accession |
P20060,Q6AXR4,P07686,P49614
|
| Protein Sub-location |
Secreted Protein/Potential Cytokines
|
| Disease from KEGG |
Metabolic pathways, Lysosome, Various types of N-glycan biosynthesis, Glycosaminoglycan degradation, Sphingolipid metabolism, Glycosphingolipid biosynthesis - globo and isoglobo series, Glycosphingolipid biosynthesis - ganglio series
|
| Gene Ensembl |
ENSECAG00000011657, ENSMUSG00000021665, ENSG00000049860, ENSCAFG00845001153, ENSBTAG00000015512, ENSMMUG00000019997
|
Pre-made viral vector of HEXB cDNA Clones/ORF Plasmid
HEXB siRNA/miRNA/oligo for RNA interfence (RNAi)
| Cat No. | Product Name | GeneID | Species | Grade | Detail |
|---|
| pGMoligo3074 | Pre-made Human HEXB/ENC-1AS/HEL-248 siRNA oligo Duplex | 3074 | Human | In-vitro grade; in-vivo grade | Detail |
| pGMoligo294673 | Pre-made Rat Hexb siRNA oligo Duplex | 294673 | Rat | In-vitro grade; in-vivo grade | Detail |
| pGMoligo15212 | Pre-made Mouse Hexb siRNA oligo Duplex | 15212 | Mouse | In-vitro grade; in-vivo grade | Detail |
| pGMoligo704464 | Pre-made Cynomolgus/Rhesus macaque HEXB siRNA oligo Duplex | 704464 | Cynomolgus/Rhesus macaque | In-vitro grade; in-vivo grade | Detail |
| pGMoligo493928 | Pre-made Cat/Feline HEXB siRNA oligo Duplex | 493928 | Cat/Feline | In-vitro grade; in-vivo grade | Detail |
| pGMoligo478100 | Pre-made Dog/Canine HEXB siRNA oligo Duplex | 478100 | Dog/Canine | In-vitro grade; in-vivo grade | Detail |
| pGMoligo618571 | Pre-made Bovines/Cattle HEXB siRNA oligo Duplex | 618571 | Bovines/Cattle | In-vitro grade; in-vivo grade | Detail |
| pGMoligo100073289 | Pre-made Equine/Horse HEXB siRNA oligo Duplex | 100073289 | Equine/Horse | In-vitro grade; in-vivo grade | Detail |
HEXB antibody/GMab
| Cat No. | Species | Antibody Name | Format | Classified by tag | Detail |
|---|
| GM-Tg-hg-SE0260-Ab | Human | Anti-Human HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-rg-SE0260-Ab | Rat | Anti-Rat HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-mg-SE0260-Ab | Mouse | Anti-Mouse HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-cynog-SE0260-Ab | Cynomolgus/Rhesus macaque | Anti-Cynomolgus/Rhesus macaque HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-felg-SE0260-Ab | Cat/Feline | Anti-Cat/Feline HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-cang-SE0260-Ab | Dog/Canine | Anti-Dog/Canine HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-bovg-SE0260-Ab | Bovines/Cattle | Anti-Bovines/Cattle HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
| GM-Tg-equg-SE0260-Ab | Equine/Horse | Anti-Equine/Horse HEXB monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
HEXB recombinant protein
| Cat No. | Species | Antigen Name | Expression Platform | Detail |
|---|
| GM-Tg-hg-SE0260-Ag | Human | Human HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-rg-SE0260-Ag | Rat | Rat HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-mg-SE0260-Ag | Mouse | Mouse HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-cynog-SE0260-Ag | Cynomolgus/Rhesus macaque | Cynomolgus/Rhesus macaque HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-felg-SE0260-Ag | Cat/Feline | Cat/Feline HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-cang-SE0260-Ag | Dog/Canine | Dog/Canine HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-bovg-SE0260-Ag | Bovines/Cattle | Bovines/Cattle HEXB recombinant protein | Mammalian cell | Detail |
| GM-Tg-equg-SE0260-Ag | Equine/Horse | Equine/Horse HEXB recombinant protein | Mammalian cell | Detail |