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Target
sublocation: Secreted Protein/Potential Cytokines.
This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, cognitive disability, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008]
Target ID |
GM-SE0222
|
Target Name |
FKRP
|
Gene Group ldentifer (Target Gene ID in Homo
species)
|
79147
|
Gene ID |
101099604 (Felis catus), 102148152 (Equus caballus), 243853 (Mus musculus), 308390 (Rattus norvegicus) 484426 (Canis lupus familiaris), 539701 (Bos taurus), 716804 (Macaca mulatta), 79147 (Homo sapiens)
|
Target Alternative Names |
FKRP,Fkrp,MDC1C,LGMD1I,A830029B19Rik,FKTR,LGMD2I,LGMDR9,MDDGA5,MDDGB5,MDDGC5
|
Uniprot Accession |
Q8CG64,Q9H9S5
|
Uniprot Entry Name |
|
Protein Sub-location |
Secreted Protein/Potential Cytokines
|
Category |
|
Disease |
|
Disease from KEGG |
Metabolic pathways, Mannose type O-glycan biosynthesis
|
Gene Ensembl |
ENSECAG00000010652, ENSMUSG00000048920, ENSCAFG00845003332, ENSMMUG00000028743, ENSG00000181027
|
Target Classification |
|
Pre-made viral vector of FKRP cDNA Clones/ORF Plasmid
FKRP siRNA/miRNA/oligo for RNA interfence (RNAi)
Cat No. | Product Name | GeneID | Species | Grade | Detail |
---|
pGMoligo79147 | Pre-made Human FKRP/FKTR/MDC1C siRNA oligo Duplex | 79147 | Human | In-vitro grade; in-vivo grade | Detail |
pGMoligo308390 | Pre-made Rat Fkrp siRNA oligo Duplex | 308390 | Rat | In-vitro grade; in-vivo grade | Detail |
pGMoligo243853 | Pre-made Mouse Fkrp/MDC1C/LGMD1I siRNA oligo Duplex | 243853 | Mouse | In-vitro grade; in-vivo grade | Detail |
pGMoligo716804 | Pre-made Cynomolgus/Rhesus macaque FKRP siRNA oligo Duplex | 716804 | Cynomolgus/Rhesus macaque | In-vitro grade; in-vivo grade | Detail |
pGMoligo101099604 | Pre-made Cat/Feline FKRP siRNA oligo Duplex | 101099604 | Cat/Feline | In-vitro grade; in-vivo grade | Detail |
pGMoligo484426 | Pre-made Dog/Canine FKRP siRNA oligo Duplex | 484426 | Dog/Canine | In-vitro grade; in-vivo grade | Detail |
pGMoligo539701 | Pre-made Bovines/Cattle FKRP siRNA oligo Duplex | 539701 | Bovines/Cattle | In-vitro grade; in-vivo grade | Detail |
pGMoligo102148152 | Pre-made Equine/Horse FKRP siRNA oligo Duplex | 102148152 | Equine/Horse | In-vitro grade; in-vivo grade | Detail |
FKRP antibody/GMab
Cat No. | Species | Antibody Name | Format | Classified by tag | Detail |
---|
GM-Tg-hg-SE0222-Ab | Human | Anti-Human FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-rg-SE0222-Ab | Rat | Anti-Rat FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-mg-SE0222-Ab | Mouse | Anti-Mouse FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-cynog-SE0222-Ab | Cynomolgus/Rhesus macaque | Anti-Cynomolgus/Rhesus macaque FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-felg-SE0222-Ab | Cat/Feline | Anti-Cat/Feline FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-cang-SE0222-Ab | Dog/Canine | Anti-Dog/Canine FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-bovg-SE0222-Ab | Bovines/Cattle | Anti-Bovines/Cattle FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
GM-Tg-equg-SE0222-Ab | Equine/Horse | Anti-Equine/Horse FKRP monoclonal antibody | mab | FACS/Biofunctional Antibody | Detail |
FKRP recombinant protein
Cat No. | Species | Antigen Name | Expression Platform | Detail |
---|
GM-Tg-hg-SE0222-Ag | Human | Human FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-rg-SE0222-Ag | Rat | Rat FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-mg-SE0222-Ag | Mouse | Mouse FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-cynog-SE0222-Ag | Cynomolgus/Rhesus macaque | Cynomolgus/Rhesus macaque FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-felg-SE0222-Ag | Cat/Feline | Cat/Feline FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-cang-SE0222-Ag | Dog/Canine | Dog/Canine FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-bovg-SE0222-Ag | Bovines/Cattle | Bovines/Cattle FKRP recombinant protein | Mammalian cell | Detail |
GM-Tg-equg-SE0222-Ag | Equine/Horse | Equine/Horse FKRP recombinant protein | Mammalian cell | Detail |