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Target
sublocation: Introcelluar Protein.
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008]
| Target ID |
GM-IP7902
|
| Target Name |
HADHA
|
Gene Group ldentifer (Target Gene ID in Homo
species)
|
3030
|
| Gene ID |
100071381 (Equus caballus), 100856745 (Canis lupus familiaris), 101084701 (Felis catus), 170670 (Rattus norvegicus) 281810 (Bos taurus), 3030 (Homo sapiens), 695975 (Macaca mulatta), 97212 (Mus musculus)
|
| Target Alternative Names |
78 kDa gastrin-binding protein,ECHA,GBP,HADH,HADHA,Hadha,LCEH,LCHAD,MTPA,Monolysocardiolipin acyltransferase,Mtpa,RGD1560655,TP-ALPHA,TP-alpha,Trifunctional enzyme subunit alpha,mitochondrial
|
| Uniprot Accession |
Q64428,P40939,Q8BMS1
|
| Protein Sub-location |
Introcelluar Protein
|
| Category |
Life Science Target
|
| Gene Ensembl |
ENSECAG00000015725, ENSCAFG00845027504, ENSBTAG00000015038, ENSG00000084754, ENSMMUG00000004380, ENSMUSG00000025745
|
Pre-made viral vector of HADHA cDNA Clones/ORF Plasmid
HADHA siRNA/miRNA/oligo for RNA interfence (RNAi)
| Cat No. | Product Name | GeneID | Species | Grade | Detail |
|---|
| pGMoligo3030 | Pre-made Human HADHA/GBP/ECHA siRNA oligo Duplex | 3030 | Human | In-vitro grade; in-vivo grade | Detail |
| pGMoligo170670 | Pre-made Rat Hadha/RGD1560655 siRNA oligo Duplex | 170670 | Rat | In-vitro grade; in-vivo grade | Detail |
| pGMoligo97212 | Pre-made Mouse Hadha/Mtpa/TP-alpha siRNA oligo Duplex | 97212 | Mouse | In-vitro grade; in-vivo grade | Detail |
| pGMoligo695975 | Pre-made Cynomolgus/Rhesus macaque HADHA siRNA oligo Duplex | 695975 | Cynomolgus/Rhesus macaque | In-vitro grade; in-vivo grade | Detail |
| pGMoligo101084701 | Pre-made Cat/Feline HADHA siRNA oligo Duplex | 101084701 | Cat/Feline | In-vitro grade; in-vivo grade | Detail |
| pGMoligo100856745 | Pre-made Dog/Canine HADHA siRNA oligo Duplex | 100856745 | Dog/Canine | In-vitro grade; in-vivo grade | Detail |
| pGMoligo281810 | Pre-made Bovines/Cattle HADHA siRNA oligo Duplex | 281810 | Bovines/Cattle | In-vitro grade; in-vivo grade | Detail |
| pGMoligo100071381 | Pre-made Equine/Horse HADHA siRNA oligo Duplex | 100071381 | Equine/Horse | In-vitro grade; in-vivo grade | Detail |
HADHA antibody/GMab
| Cat No. | Species | Antibody Name | Format | Classified by tag | Detail |
|---|
| GM-Tg-hg-IP7902-Ab | Human | Anti-Human HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-rg-IP7902-Ab | Rat | Anti-Rat HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-mg-IP7902-Ab | Mouse | Anti-Mouse HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-cynog-IP7902-Ab | Cynomolgus/Rhesus macaque | Anti-Cynomolgus/Rhesus macaque HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-felg-IP7902-Ab | Cat/Feline | Anti-Cat/Feline HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-cang-IP7902-Ab | Dog/Canine | Anti-Dog/Canine HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-bovg-IP7902-Ab | Bovines/Cattle | Anti-Bovines/Cattle HADHA monoclonal antibody | mab | | Detail |
| GM-Tg-equg-IP7902-Ab | Equine/Horse | Anti-Equine/Horse HADHA monoclonal antibody | mab | | Detail |
HADHA recombinant protein
| Cat No. | Species | Antigen Name | Expression Platform | Detail |
|---|
| GM-Tg-hg-IP7902-Ag | Human | Human HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-rg-IP7902-Ag | Rat | Rat HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-mg-IP7902-Ag | Mouse | Mouse HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-cynog-IP7902-Ag | Cynomolgus/Rhesus macaque | Cynomolgus/Rhesus macaque HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-felg-IP7902-Ag | Cat/Feline | Cat/Feline HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-cang-IP7902-Ag | Dog/Canine | Dog/Canine HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-bovg-IP7902-Ag | Bovines/Cattle | Bovines/Cattle HADHA recombinant protein | Mammalian cell | Detail |
| GM-Tg-equg-IP7902-Ag | Equine/Horse | Equine/Horse HADHA recombinant protein | Mammalian cell | Detail |