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Target
sublocation: Introcelluar Protein.
The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the ALD subfamily, which is involved in peroxisomal import of fatty acids and/or fatty acyl-CoAs in the organelle. All known peroxisomal ABC transporters are half transporters which require a partner half transporter molecule to form a functional homodimeric or heterodimeric transporter. The function of this peroxisomal membrane protein is unknown; however this protein is speculated to function as a dimerization partner of ABCD1 and/or other peroxisomal ABC transporters. Mutations in this gene have been observed in patients with adrenoleukodystrophy, a severe demyelinating disease. This gene has been identified as a candidate for a modifier gene, accounting for the extreme variation among adrenoleukodystrophy phenotypes. This gene is also a candidate for a complement group of Zellweger syndrome, a genetically heterogeneous disorder of peroxisomal biogenesis. [provided by RefSeq, Jul 2008]
| Target ID |
GM-IP0282
|
| Target Name |
ABCD2
|
Gene Group ldentifer (Target Gene ID in Homo
species)
|
225
|
| Gene ID |
100070407 (Equus caballus), 101095424 (Felis catus), 225 (Homo sapiens), 26874 (Mus musculus) 477643 (Canis lupus familiaris), 526436 (Bos taurus), 697556 (Macaca mulatta), 84356 (Rattus norvegicus)
|
| Target Alternative Names |
ABC39,ABCD2,ALDL1,ALDR,ALDRP,ATP-binding cassette sub-family D member 2,Abcd2,Adrenoleukodystrophy-like 1,Adrenoleukodystrophy-related protein (hALDR),hALDR
|
| Uniprot Accession |
Q9UBJ2,Q61285,Q9QY44
|
| Protein Sub-location |
Introcelluar Protein
|
| Disease from KEGG |
ABC transporters
|
| Gene Ensembl |
ENSG00000173208, ENSMUSG00000055782, ENSCAFG00845030727, ENSMMUG00000014007
|
Pre-made viral vector of ABCD2 cDNA Clones/ORF Plasmid
ABCD2 siRNA/miRNA/oligo for RNA interfence (RNAi)
| Cat No. | Product Name | GeneID | Species | Grade | Detail |
|---|
| pGMoligo225 | Pre-made Human ABCD2/ALDR/ABC39 siRNA oligo Duplex | 225 | Human | In-vitro grade; in-vivo grade | Detail |
| pGMoligo84356 | Pre-made Rat Abcd2/ALDR siRNA oligo Duplex | 84356 | Rat | In-vitro grade; in-vivo grade | Detail |
| pGMoligo26874 | Pre-made Mouse Abcd2/ALDR/ABC39 siRNA oligo Duplex | 26874 | Mouse | In-vitro grade; in-vivo grade | Detail |
| pGMoligo697556 | Pre-made Cynomolgus/Rhesus macaque ABCD2 siRNA oligo Duplex | 697556 | Cynomolgus/Rhesus macaque | In-vitro grade; in-vivo grade | Detail |
| pGMoligo101095424 | Pre-made Cat/Feline ABCD2 siRNA oligo Duplex | 101095424 | Cat/Feline | In-vitro grade; in-vivo grade | Detail |
| pGMoligo477643 | Pre-made Dog/Canine ABCD2 siRNA oligo Duplex | 477643 | Dog/Canine | In-vitro grade; in-vivo grade | Detail |
| pGMoligo526436 | Pre-made Bovines/Cattle ABCD2 siRNA oligo Duplex | 526436 | Bovines/Cattle | In-vitro grade; in-vivo grade | Detail |
| pGMoligo100070407 | Pre-made Equine/Horse ABCD2 siRNA oligo Duplex | 100070407 | Equine/Horse | In-vitro grade; in-vivo grade | Detail |
ABCD2 antibody/GMab
| Cat No. | Species | Antibody Name | Format | Classified by tag | Detail |
|---|
| GM-Tg-hg-IP0282-Ab | Human | Anti-Human ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-rg-IP0282-Ab | Rat | Anti-Rat ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-mg-IP0282-Ab | Mouse | Anti-Mouse ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-cynog-IP0282-Ab | Cynomolgus/Rhesus macaque | Anti-Cynomolgus/Rhesus macaque ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-felg-IP0282-Ab | Cat/Feline | Anti-Cat/Feline ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-cang-IP0282-Ab | Dog/Canine | Anti-Dog/Canine ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-bovg-IP0282-Ab | Bovines/Cattle | Anti-Bovines/Cattle ABCD2 monoclonal antibody | mab | | Detail |
| GM-Tg-equg-IP0282-Ab | Equine/Horse | Anti-Equine/Horse ABCD2 monoclonal antibody | mab | | Detail |
ABCD2 recombinant protein
| Cat No. | Species | Antigen Name | Expression Platform | Detail |
|---|
| GM-Tg-hg-IP0282-Ag | Human | Human ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-rg-IP0282-Ag | Rat | Rat ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-mg-IP0282-Ag | Mouse | Mouse ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-cynog-IP0282-Ag | Cynomolgus/Rhesus macaque | Cynomolgus/Rhesus macaque ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-felg-IP0282-Ag | Cat/Feline | Cat/Feline ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-cang-IP0282-Ag | Dog/Canine | Dog/Canine ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-bovg-IP0282-Ag | Bovines/Cattle | Bovines/Cattle ABCD2 recombinant protein | Mammalian cell | Detail |
| GM-Tg-equg-IP0282-Ag | Equine/Horse | Equine/Horse ABCD2 recombinant protein | Mammalian cell | Detail |