Explore PAH gene products and cross-species
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insights for Homo sapiens (human), Cynomolgus monkeys, rodents
(mouse/rat), canines, felines, bovines, and equines. Your
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Target
sublocation: Introcelluar Protein.
This gene encodes a member of the biopterin-dependent aromatic amino acid hydroxylase protein family. The encoded phenylalanine hydroxylase enzyme hydroxylates phenylalanine to tyrosine and is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [provided by RefSeq, Aug 2017]
| Target ID |
GM-T76213
|
| Target Name |
PAH
|
Gene Group ldentifer (Target Gene ID in Homo
species)
|
5053
|
| Gene ID |
100053361 (Equus caballus), 101081741 (Felis catus), 18478 (Mus musculus), 24616 (Rattus norvegicus) 475446 (Canis lupus familiaris), 5053 (Homo sapiens), 510583 (Bos taurus), 698696 (Macaca mulatta)
|
| Target Alternative Names |
PAH,PH,PKU,PKU1,Pah,Phe-4-monooxygenase,Phenylalanine-4-hydroxylase
|
| Uniprot Accession |
P16331,P04176,P00439,Q2KIH7
|
| Protein Sub-location |
Introcelluar Protein
|
| Category |
Therapeutics Target
|
| Disease from KEGG |
Metabolic pathways
|
| Gene Ensembl |
ENSECAG00000019047, ENSMUSG00000020051, ENSCAFG00845009553, ENSG00000171759, ENSBTAG00000012794, ENSMMUG00000011908
|
Pre-made viral vector of PAH cDNA Clones/ORF Plasmid
PAH siRNA/miRNA/oligo for RNA interfence (RNAi)
| Cat No. | Product Name | GeneID | Species | Grade | Detail |
|---|
| pGMoligo5053 | Pre-made Human PAH/PH/PKU siRNA oligo Duplex | 5053 | Human | In-vitro grade; in-vivo grade | Detail |
| pGMoligo24616 | Pre-made Rat Pah siRNA oligo Duplex | 24616 | Rat | In-vitro grade; in-vivo grade | Detail |
| pGMoligo18478 | Pre-made Mouse Pah siRNA oligo Duplex | 18478 | Mouse | In-vitro grade; in-vivo grade | Detail |
| pGMoligo698696 | Pre-made Cynomolgus/Rhesus macaque PAH siRNA oligo Duplex | 698696 | Cynomolgus/Rhesus macaque | In-vitro grade; in-vivo grade | Detail |
| pGMoligo101081741 | Pre-made Cat/Feline PAH siRNA oligo Duplex | 101081741 | Cat/Feline | In-vitro grade; in-vivo grade | Detail |
| pGMoligo475446 | Pre-made Dog/Canine PAH siRNA oligo Duplex | 475446 | Dog/Canine | In-vitro grade; in-vivo grade | Detail |
| pGMoligo510583 | Pre-made Bovines/Cattle PAH siRNA oligo Duplex | 510583 | Bovines/Cattle | In-vitro grade; in-vivo grade | Detail |
| pGMoligo100053361 | Pre-made Equine/Horse PAH siRNA oligo Duplex | 100053361 | Equine/Horse | In-vitro grade; in-vivo grade | Detail |
PAH antibody/GMab
| Cat No. | Species | Antibody Name | Format | Classified by tag | Detail |
|---|
| GM-Tg-hg-T76213-Ab | Human | Anti-Human PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-rg-T76213-Ab | Rat | Anti-Rat PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-mg-T76213-Ab | Mouse | Anti-Mouse PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-cynog-T76213-Ab | Cynomolgus/Rhesus macaque | Anti-Cynomolgus/Rhesus macaque PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-felg-T76213-Ab | Cat/Feline | Anti-Cat/Feline PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-cang-T76213-Ab | Dog/Canine | Anti-Dog/Canine PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-bovg-T76213-Ab | Bovines/Cattle | Anti-Bovines/Cattle PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
| GM-Tg-equg-T76213-Ab | Equine/Horse | Anti-Equine/Horse PAH monoclonal antibody | mab | Therapeutics Target antibody | Detail |
PAH recombinant protein
| Cat No. | Species | Antigen Name | Expression Platform | Detail |
|---|
| GM-Tg-hg-T76213-Ag | Human | Human PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-rg-T76213-Ag | Rat | Rat PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-mg-T76213-Ag | Mouse | Mouse PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-cynog-T76213-Ag | Cynomolgus/Rhesus macaque | Cynomolgus/Rhesus macaque PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-felg-T76213-Ag | Cat/Feline | Cat/Feline PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-cang-T76213-Ag | Dog/Canine | Dog/Canine PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-bovg-T76213-Ag | Bovines/Cattle | Bovines/Cattle PAH recombinant protein | Mammalian cell | Detail |
| GM-Tg-equg-T76213-Ag | Equine/Horse | Equine/Horse PAH recombinant protein | Mammalian cell | Detail |