Explore SGSH gene products and cross-species
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biological information, expression tools, and therapeutic
insights for Homo sapiens (human), Cynomolgus monkeys, rodents
(mouse/rat), canines, felines, bovines, and equines. Your
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Target
sublocation: Secreted Protein/Potential Cytokines.
This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
| Target ID |
GM-T64645
|
| Target Name |
SGSH
|
Gene Group ldentifer (Target Gene ID in Homo
species)
|
6448
|
| Gene ID |
100056499 (Equus caballus), 101094715 (Felis catus), 27029 (Mus musculus), 403707 (Canis lupus familiaris) 535442 (Bos taurus), 6448 (Homo sapiens), 688293 (Rattus norvegicus), 717977 (Macaca mulatta)
|
| Target Alternative Names |
4632406A19Rik,HSS,MPS3A,N-sulphoglucosamine sulphohydrolase,SFMD,SGSH,Sgsh,Sulfoglucosamine sulfamidase,Sulphamidase
|
| Uniprot Accession |
P51688
|
| Protein Sub-location |
Secreted Protein/Potential Cytokines
|
| Category |
Therapeutics Target
|
| Disease from KEGG |
Metabolic pathways, Lysosome, Glycosaminoglycan degradation
|
| Gene Ensembl |
ENSECAG00000004844, ENSMUSG00000005043, ENSCAFG00845013218, ENSBTAG00000015267, ENSG00000181523, ENSMMUG00000002849
|
SGSH siRNA/miRNA/oligo for RNA interfence (RNAi)
| Cat No. | Product Name | GeneID | Species | Grade | Detail |
|---|
| pGMoligo6448 | Pre-made Human SGSH/HSS/SFMD siRNA oligo Duplex | 6448 | Human | In-vitro grade; in-vivo grade | Detail |
| pGMoligo688293 | Pre-made Rat Sgsh siRNA oligo Duplex | 688293 | Rat | In-vitro grade; in-vivo grade | Detail |
| pGMoligo27029 | Pre-made Mouse Sgsh/4632406A19Rik siRNA oligo Duplex | 27029 | Mouse | In-vitro grade; in-vivo grade | Detail |
| pGMoligo717977 | Pre-made Cynomolgus/Rhesus macaque SGSH siRNA oligo Duplex | 717977 | Cynomolgus/Rhesus macaque | In-vitro grade; in-vivo grade | Detail |
| pGMoligo101094715 | Pre-made Cat/Feline SGSH siRNA oligo Duplex | 101094715 | Cat/Feline | In-vitro grade; in-vivo grade | Detail |
| pGMoligo403707 | Pre-made Dog/Canine SGSH/HSS siRNA oligo Duplex | 403707 | Dog/Canine | In-vitro grade; in-vivo grade | Detail |
| pGMoligo535442 | Pre-made Bovines/Cattle SGSH siRNA oligo Duplex | 535442 | Bovines/Cattle | In-vitro grade; in-vivo grade | Detail |
| pGMoligo100056499 | Pre-made Equine/Horse SGSH siRNA oligo Duplex | 100056499 | Equine/Horse | In-vitro grade; in-vivo grade | Detail |
SGSH antibody/GMab
| Cat No. | Species | Antibody Name | Format | Classified by tag | Detail |
|---|
| GM-Tg-hg-T64645-Ab | Human | Anti-Human SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-rg-T64645-Ab | Rat | Anti-Rat SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-mg-T64645-Ab | Mouse | Anti-Mouse SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-cynog-T64645-Ab | Cynomolgus/Rhesus macaque | Anti-Cynomolgus/Rhesus macaque SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-felg-T64645-Ab | Cat/Feline | Anti-Cat/Feline SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-cang-T64645-Ab | Dog/Canine | Anti-Dog/Canine SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-bovg-T64645-Ab | Bovines/Cattle | Anti-Bovines/Cattle SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
| GM-Tg-equg-T64645-Ab | Equine/Horse | Anti-Equine/Horse SGSH monoclonal antibody | mab | FACS/Biofunctional Antibody, Therapeutics Target antibody | Detail |
SGSH recombinant protein
| Cat No. | Species | Antigen Name | Expression Platform | Detail |
|---|
| GM-Tg-hg-T64645-Ag | Human | Human SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-rg-T64645-Ag | Rat | Rat SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-mg-T64645-Ag | Mouse | Mouse SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-cynog-T64645-Ag | Cynomolgus/Rhesus macaque | Cynomolgus/Rhesus macaque SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-felg-T64645-Ag | Cat/Feline | Cat/Feline SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-cang-T64645-Ag | Dog/Canine | Dog/Canine SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-bovg-T64645-Ag | Bovines/Cattle | Bovines/Cattle SGSH recombinant protein | Mammalian cell | Detail |
| GM-Tg-equg-T64645-Ag | Equine/Horse | Equine/Horse SGSH recombinant protein | Mammalian cell | Detail |