BCKDHA Target & Gene Products-cDNA ORF clones/siRNA/antibody/protein

Explore BCKDHA gene products and cross-species research data at TarMart platform. Discover comprehensive biological information, expression tools, and therapeutic insights for Homo sapiens (human), Cynomolgus monkeys, rodents (mouse/rat), canines, felines, bovines, and equines. Your premier destination for multi-species gene research solutions
Target sublocation: Introcelluar Protein.
The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Sep 2009]

Target ID GM-IP10864
Target Name BCKDHA
Gene Group ldentifer
(Target Gene ID in Homo species)
593
Gene ID 100068678 (Equus caballus), 101087186 (Felis catus), 106994773 (Macaca mulatta), 12039 (Mus musculus)
25244 (Rattus norvegicus), 282149 (Bos taurus), 484488 (Canis lupus familiaris), 593 (Homo sapiens)
Target Alternative Names 2-oxoisovalerate dehydrogenase subunit alpha,BCKAD,BCKDA,BCKDE1A,BCKDH E1-alpha),BCKDHA,Bckdha,Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain (BCKDE1A,E1[a],E1a,MSU,MSUD1,MSUD1A,OVD1A,mitochondrial
Uniprot Accession P50136,P11960,P11178,P12694
Protein Sub-location Introcelluar Protein
Category Life Science Target
Gene Ensembl ENSECAG00000012246, ENSMMUG00000014346, ENSMUSG00000060376, ENSBTAG00000016037, ENSCAFG00845002258, ENSG00000248098


Pre-made viral vector of BCKDHA cDNA Clones/ORF Plasmid

Cat No.Product NameNMIDGeneIDSpeciesTypeMarkerFusion TagPromoterDetail
pGMLP001457Human BCKDHA/BCKDE1A/MSU Lentivirus plasmidNM_000709593HumanLentivirus plasmidZsGreen3xflag (C-Terminal)CMVDetail
vGMLP001457Human BCKDHA/BCKDE1A/MSU Lentivirus particleNM_000709593HumanLentivirus particleZsGreen3xflag (C-Terminal)CMVDetail
pGMLPm001848Mouse Bckdha Lentivirus plasmidNM_00753312039MouseLentivirus plasmidZsGreen3xflag (C-Terminal)CMVDetail
vGMLPm001848Mouse Bckdha Lentivirus particleNM_00753312039MouseLentivirus particleZsGreen3xflag (C-Terminal)CMVDetail


BCKDHA siRNA/miRNA/oligo for RNA interfence (RNAi)

Cat No.Product NameGeneIDSpeciesGradeDetail
pGMoligo593Pre-made Human BCKDHA/MSU/MSUD1 siRNA oligo Duplex593HumanIn-vitro grade; in-vivo gradeDetail
pGMoligo25244Pre-made Rat Bckdha/E1a/BCKDA siRNA oligo Duplex25244RatIn-vitro grade; in-vivo gradeDetail
pGMoligo12039Pre-made Mouse Bckdha/BCKAD/E1[a] siRNA oligo Duplex12039MouseIn-vitro grade; in-vivo gradeDetail
pGMoligo106994773Pre-made Cynomolgus/Rhesus macaque BCKDHA siRNA oligo Duplex106994773Cynomolgus/Rhesus macaqueIn-vitro grade; in-vivo gradeDetail
pGMoligo101087186Pre-made Cat/Feline BCKDHA siRNA oligo Duplex101087186Cat/FelineIn-vitro grade; in-vivo gradeDetail
pGMoligo484488Pre-made Dog/Canine BCKDHA siRNA oligo Duplex484488Dog/CanineIn-vitro grade; in-vivo gradeDetail
pGMoligo282149Pre-made Bovines/Cattle BCKDHA siRNA oligo Duplex282149Bovines/CattleIn-vitro grade; in-vivo gradeDetail
pGMoligo100068678Pre-made Equine/Horse BCKDHA siRNA oligo Duplex100068678Equine/HorseIn-vitro grade; in-vivo gradeDetail


BCKDHA antibody/GMab

Cat No.SpeciesAntibody NameFormatClassified by tagDetail
GM-Tg-hg-IP10864-AbHumanAnti-Human BCKDHA monoclonal antibodymabDetail
GM-Tg-rg-IP10864-AbRatAnti-Rat BCKDHA monoclonal antibodymabDetail
GM-Tg-mg-IP10864-AbMouseAnti-Mouse BCKDHA monoclonal antibodymabDetail
GM-Tg-cynog-IP10864-AbCynomolgus/Rhesus macaqueAnti-Cynomolgus/Rhesus macaque BCKDHA monoclonal antibodymabDetail
GM-Tg-felg-IP10864-AbCat/FelineAnti-Cat/Feline BCKDHA monoclonal antibodymabDetail
GM-Tg-cang-IP10864-AbDog/CanineAnti-Dog/Canine BCKDHA monoclonal antibodymabDetail
GM-Tg-bovg-IP10864-AbBovines/CattleAnti-Bovines/Cattle BCKDHA monoclonal antibodymabDetail
GM-Tg-equg-IP10864-AbEquine/HorseAnti-Equine/Horse BCKDHA monoclonal antibodymabDetail


BCKDHA recombinant protein

Cat No.SpeciesAntigen NameExpression PlatformDetail
GM-Tg-hg-IP10864-AgHumanHuman BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-rg-IP10864-AgRatRat BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-mg-IP10864-AgMouseMouse BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-cynog-IP10864-AgCynomolgus/Rhesus macaqueCynomolgus/Rhesus macaque BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-felg-IP10864-AgCat/FelineCat/Feline BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-cang-IP10864-AgDog/CanineDog/Canine BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-bovg-IP10864-AgBovines/CattleBovines/Cattle BCKDHA recombinant proteinMammalian cellDetail
GM-Tg-equg-IP10864-AgEquine/HorseEquine/Horse BCKDHA recombinant proteinMammalian cellDetail